Pachydermoperiostosis (Primary Hypertrophic Osteoarthropathy): Case Report
نویسندگان
چکیده
syndrome consisting of clubbing of the digits of the hands and feet, enlargement of the extremities secondary to periarticular and osseous proliferation, and painful and swollen joints. The condition has been divided into two categories, primary hypertrophic osteoarthropathy, also known as “pachydermoperiostosis”, and secondary hypertrophic osteoarthropathy, frequently referred to as “hypertrophic pulmonary osteoarthropathy” due to its association with a variety of pulmonary causes. Recent reports have described the findings of magnetic resonance imaging and bone scintigraphy(1-4). We report a case of pachydermoperiostosis, describing the imaging features apparent at plain radiography, bone scintigraphy, and magnetic resonance imaging. J Korean Radiol Soc 2002;47:533-538
منابع مشابه
Hypertrophy of the feet and ankles presenting in primary hypertrophic osteoarthropathy or pachydermoperiostosis: a case report
INTRODUCTION Pachydermoperiostosis or primary hypertrophic osteoathropathy is a rare genetic disease with autosomal transmission. This disorder, which affects both bones and skin, is characterized by the association of dermatologic changes (pachydermia or thickening of the skin) and rheumatologic manifestations (periostosis and finger clubbing). Here, we report a new observation of pachydermope...
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